Ocular manifestations in patient with congenital erythropoietic porphyria

Isanta-Otal, C. ; López-Valverde, G. (Universidad de Zaragoza) ; Mateo Orobia, A.J. (Universidad de Zaragoza) ; Pablo, L.E. (Universidad de Zaragoza)

Resumen: We present the case of a 52-year-old woman referred to our service because of extreme ocular surface dryness. The patient showed corneal, conjunctival, and eyelid manifestations of ocular congenital erythropoietic porphyria (CEP). We started treatment with autologous serum, topical steroids, and cyclosporine twice a day, topical retinoids, and intense corneal lubrication. The patient referred significant improvement of ocular bothering and less discomfort since treatment was initiated. We describe the management of the herewith presented case of ocular CEP. © 2019 Indian Journal of Ophthalmology.

Idioma: Inglés

DOI: 10.4103/ijo.IJO_1776_18

Año: 2019

Publicado en: INDIAN JOURNAL OF OPHTHALMOLOGY 67, 10 (2019), 1765-1768
ISSN: 0301-4738

Factor impacto JCR: 1.25 (2019)

Categ. JCR: OPHTHALMOLOGY rank: 52 / 60 = 0.867 (2019) - Q4 - T3

Factor impacto SCIMAGO: 0.482 - Ophthalmology (Q3)

Tipo y forma: Article (Published version)

Área (Departamento): Área Oftalmología (Dpto. Cirugía,Ginecol.Obstetr.)